Desmoid tumor

Desmoid tumor Microchapters
Home
Patient Information
Overview
Historical Perspective
Classification
Pathophysiology
Causes
Differentiating Desmoid tumor from other Diseases
Epidemiology and Demographics
Risk Factors
Natural History, Complications and Prognosis
Diagnosis
History and Symptoms
Physical Examination
Laboratory Findings
CT
MRI
Other Imaging Findings
Other Diagnostic Studies
Treatment
Medical Therapy
Surgery
Cost-Effectiveness of Therapy
Future or Investigational Therapies
Case Studies
Case #1

WikiDoc Resources for Desmoid tumor
Articles
Most recent articles on Desmoid tumor Most cited articles on Desmoid tumor Review articles on Desmoid tumor Articles on Desmoid tumor in N Eng J Med, Lancet, BMJ
Media
Powerpoint slides on Desmoid tumor Images of Desmoid tumor Photos of Desmoid tumor Podcasts & MP3s on Desmoid tumor Videos on Desmoid tumor
Evidence Based Medicine
Cochrane Collaboration on Desmoid tumor Bandolier on Desmoid tumor TRIP on Desmoid tumor
Clinical Trials
Ongoing Trials on Desmoid tumor at Clinical Trials.gov Trial results on Desmoid tumor Clinical Trials on Desmoid tumor at Google
Guidelines / Policies / Govt
US National Guidelines Clearinghouse on Desmoid tumor NICE Guidance on Desmoid tumor NHS PRODIGY Guidance FDA on Desmoid tumor CDC on Desmoid tumor
Books
Books on Desmoid tumor
News
Desmoid tumor in the news Be alerted to news on Desmoid tumor News trends on Desmoid tumor
Commentary
Blogs on Desmoid tumor
Definitions
Definitions of Desmoid tumor
Patient Resources / Community
Patient resources on Desmoid tumor Discussion groups on Desmoid tumor Patient Handouts on Desmoid tumor Directions to Hospitals Treating Desmoid tumor Risk calculators and risk factors for Desmoid tumor
Healthcare Provider Resources
Symptoms of Desmoid tumor Causes & Risk Factors for Desmoid tumor Diagnostic studies for Desmoid tumor Treatment of Desmoid tumor
Continuing Medical Education (CME)
CME Programs on Desmoid tumor
International
Desmoid tumor en Espanol Desmoid tumor en Francais
Business
Desmoid tumor in the Marketplace Patents on Desmoid tumor
Experimental / Informatics
List of terms related to Desmoid tumor

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Synonyms and keywords: Aggressive fibromatosis

Overview

A desmoid tumor (sometimes referred to as aggressive fibromatosis) is a rare (3 per million population) tumor that may or may not be part of a genetic syndrome such as familial adenomatous polyposis (FAP).

Classification

Desmoid tumors may be classified as extra-abdominal, abdominal wall, or intra-abdominal (the last is more common in patients with FAP). It is thought that the lesions may develop in relation to estrogen levels or trauma/operations.

Pathophysiology

Microscopic Pathology

Histologically, Desmoid tumors resemble low-grade fibrosarcomas, but they are very infiltrative and tend to recur even after complete resection (systemic metastasis is rare).

Treatment

Treatment may consist of watching and waiting, complete surgical removal, radiation therapy, antiestrogens and NSAIDs, or chemotherapy.

External links

• Desmoid Tumor Research Foundation