Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Hannan Javed, M.D.[2]
Overview
Vascular Anomalies
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Vascular Tumors
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Vascular Malformations
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Benign
Locally aggressive or
Borderline
Malignant
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Simple
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Combined°
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of major named vessels
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associated with other anomalies
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Capillary malformations
Lymphatic malformations
Venous malformations
Arteriovenous malformations*
Arteriovenous fistula*
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Capillary venous malformation , Capillary lymphatic malformation
Lymphatic venous malformation, Capillary lymphatic venous malformation
Capillary arteriovenous malformation
Capillary lymphatic arteriovenous malformation
others
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See details
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See list
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° defined as two or more vascular malformations found in one lesion
* high flow lesions
Classification
Classification of Vascular Malformations
| | | | | | | | | | | | | | | | | | | | | | | Vascular malformations | | | | | | | | | | | | | | | | | | | | | |
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| | | | | | | Simple | | | | | | | | Combined | | | | | | | | | | of major named vessels | | | | | | | | asscoiated with other anomalies | | | | | |
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| | | | | | | | | | | | | | | | | | Combined vascular malformations*
CM + VM | Capillary-venous malformation | CVM |
CM + LM | Capillary-lymphatic malformation | CLM |
CM + AVM | Capillary-arteriovenous malformation | CAVM |
LM + VM | Lymphatic-venous malformation | LVM |
CM + LM + VM | Capillary-lymphatic-venous malformation | CLVM |
CM + LM + AVM | Capillary-lymphatic-arteriovenous malformation | CLVM |
CM + VM + AVM | Capillary-venous-arteriovenous malformation | CVAVM |
CM + LM + VM + AVM | Capillary-lymphatic-venous-arteriovenous malformation | CLVAVM |
| | | | | | | | | | Anomalies of major named vessels (also known as "channel type" or "truncal" vascular malformations) | | | | | | | | Vascular malformations associated with other anomalies
Klippel-Trenaunay syndrome | CM + VM +/-LM + limb overgrowth |
Parke's Weber syndrome | CM + AVF + limb overgrowth |
Servelle-Martorell syndrome | Limb VM + bone undergrowth |
Sturge-Weber syndrome | Facial + leptomeningeal CM + eye anomalies
+/-bone and/or soft tissue overgrowth |
Maffucci syndrome | VM +/-spindle-cell hemangioma + enchondroma |
Limb CM + congenital non-progressive limb overgrowth | |
Macrocephaly-CM (M-CM / MCAP) | |
Microcephaly-CM (MICCAP) | |
CLOVES syndrome | LM + VM + CM +/-AVM+ lipomatous overgrowth |
Proteus syndrome | CM, VM and/or LM + asymmetrical somatic overgrowth |
Bannayan-Riley-Ruvalcaba sd | lower lip CM + face and neck LM + asymmetry and partial/generalized overgrowth |
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| | Capillary malformations | | | Lymphatic malformations | | | Venous malformations | | | Arteriovenous malformations | | | Arteriovenous fistula | | | | | | | | | | | | | | | | | | | | | | |
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| | | | {{{ D03 }}} | | | | {{{ E03 }}} | | | | {{{ F03 }}} | | | | {{{ G03 }}} | | | | {{{ H03 }}} | | | | | | | | | | | | | | | | | | | | | | |
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| | | | {{{ D07 }}} | | | | {{{ E07 }}} | | | | {{{ F07 }}} | | | | | | | | | | | | | | | | | | | | | | | | | | | | | | | | |
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Tables
Anomalies of major named vessels
(also known as "channel type" or "truncal" vascular malformations)
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Affect
lymphatics
veins
arteries
Anomalies of
origin
course
number
length
diameter (aplasia, hypoplasia, stenosis, ectasia / aneurysm)
valves
communication (AVF)
persistence (of embryonal vessel)
Combined vascular malformations*
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CM + VM
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capillary-venous malformation
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CVM
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CM + LM
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capillary-lymphatic malformation
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CLM
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CM + AVM
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capillary-arteriovenous malformation
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CAVM
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LM + VM
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lymphatic-venous malformation
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LVM
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CM + LM + VM
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capillary-lymphatic-venous malformation
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CLVM
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CM + LM + AVM
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capillary-lymphatic-arteriovenous malformation
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CLAVM
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CM + VM + AVM
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capillary-venous-arteriovenous malformation
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CVAVM
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CM + LM + VM + AVM
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capillary-lymphatic-venous-arteriovenous m.
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CLVAVM
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Vascular malformations associated with other anomalies
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Klippel-Trenaunay syndrome *
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CM + VM +/-LM + limb overgrowth
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Parkes Weber syndrome
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CM + AVF + limb overgrowth
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Servelle-Martorell syndrome
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limb VM + bone undergrowth
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Sturge-Weber syndrome
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facial + leptomeningeal CM + eye anomalies
+/-bone and/or soft tissue overgrowth
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Limb CM + congenital non-progressive limb overgrowth
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Maffucci syndrome
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VM +/-spindle-cell hemangioma + enchondroma
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Macrocephaly-CM (M-CM / MCAP) *
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Microcephaly-CM (MICCAP)
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CLOVES syndrome *
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LM + VM + CM +/-AVM+ lipomatous overgrowth
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Proteus syndrome
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CM, VM and/or LM + asymmetrical somatic overgrowth
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Bannayan-Riley-Ruvalcaba sd
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lower lip CM + face and neck LM + asymmetry and partial/generalized overgrowth
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Pathogenesis of xxx disease is due to:
Physiology
Medical Therapy
Naural History
Historical Perspective
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