Desmoid tumor surgery

Desmoid tumor Microchapters
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Case #1

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Sara Mohsin, M.D.[2]Faizan Sheraz, M.D. [3]

Overview

Surgical resection is not recommended among patients with advanced or metastatic malignancy.

Surgery

• Surgical resection is not recommended among patients with advanced or metastatic malignancy.
• Desmoid tumor does not have any propensity for metastasis although it may aggressively invade structures.
• The optimal management for aggressive fibromatosis depends on tumor location and extent.
• Surgical resection may be offered although the likelihood of local recurrence after surgery is high, particularly if margins are positive.
• Wide local excision followed by reconstruction of the defect is the treatment of choice.
• Full-thickness resection of the tumor-containing abdominal wall with a grossly negative margin has to be performed when the lesion closely approximates or involves the peritoneum.
• Intraperitoneal organs or adjacent bony structures involved by tumor must be resected as well.
• Incomplete tumor removal or involved excision margins may lead to local recurrence.
• It is estimated that 25 to 40% of patients who undergo surgery can have a local recurrence