Eisenmenger’s syndrome surgery
Eisenmenger’s syndrome Microchapters |
Diagnosis |
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Eisenmenger’s syndrome ACC/AHA Guidelines for Evaluation of Patients |
Treatment |
Eisenmenger’s syndrome surgery On the Web |
American Roentgen Ray Society Images of Eisenmenger’s syndrome surgery |
Risk calculators and risk factors for Eisenmenger’s syndrome surgery |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Abdelrahman Ibrahim Abushouk, MD[2], Cafer Zorkun, M.D., Ph.D. [3]
Overview
Congenital heart defects should undergo surgical repair before progression to Eisenmenger's syndrome. Once the condition develops into Eisenmenger's syndrome, no surgical cure is available except for heart and lung transplantation. However, palliative interventions (as creation of an artificial ASD) may prolong the lifespan and improve the quality of life.
Surgery
- Congenital heart defects should undergo surgical repair before progression to Eisenmenger's syndrome.[1]
- Once the condition develops into Eisenmenger's syndrome, no surgical cure is available except for heart and lung transplantation.
- This is because the defect itself may prevent worsening of the pulmonary vascular resistance in the face of increasing right ventricular pressure.
- However, palliative interventions may prolong the lifespan and improve the quality of life.
- For example, creation of an artificial ASD can decompress the high systolic right ventricular pressure in patients with suprasystemic pulmonary artery pressures and impending right ventricular failure.
- In children, pulmonary vascular resistance > 6 Woods units/m2 and poor vasodilator response are predictors of post-surgical complications as right heart failure, pulmonary hypertension, and hypertensive crises.
- However, surgery in general is though to lack benefit with a plethora of potential complications.
References
- ↑ Stout KK, Daniels CJ, Aboulhosn JA, Bozkurt B, Broberg CS, Colman JM et al. (2019) 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. Circulation 139 (14):e698-e800. DOI:10.1161/CIR.0000000000000603 PMID: 30586767