Tricuspid atresia natural history, complications and prognosis

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor-In-Chief:Sara Zand, M.D.[2] Keri Shafer, M.D. [3] Priyamvada Singh, MBBS [4] Assistant Editor-In-Chief: Kristin Feeney, B.S. [5]

Natural History, Complications and Prognosis

Early clinical features in infants include cyanosis of lips and tongue, difficulty in breathing, tiring easily during feeding.
The severity of cyanosis in infants with pulmonary stenosis is dependent on the amount of pulmonary blood flow passing throughpatent ductus arteriosus.
After physiologic closure of patent ductus arteriosus (PDA), the cyanosis will be aggravated.
In patients with normal pulmonary blood flow, complications of heart failure may occur.
Prognosis is generally poor without surgery and 90% of patients will die before 10 years old.
The 15-year survival of patients with Fontan procedure is approximately %92.^[1]

↑ Mery, Carlos M.; De León, Luis E.; Trujillo-Diaz, Daniel; Ocampo, Elena C.; Dickerson, Heather A.; Zhu, Huirong; Adachi, Iki; Heinle, Jeffrey S.; Fraser, Charles D.; Ermis, Peter R. (2019). "Contemporary Outcomes of the Fontan Operation: A Large Single-Institution Cohort". The Annals of Thoracic Surgery. 108 (5): 1439–1446. doi:10.1016/j.athoracsur.2019.05.039. ISSN 0003-4975.
↑ Fredenburg, Tyler B.; Johnson, Tiffanie R.; Cohen, Mervyn D. (2011). "The Fontan Procedure: Anatomy, Complications, and Manifestations of Failure". RadioGraphics. 31 (2): 453–463. doi:10.1148/rg.312105027. ISSN 0271-5333.