Pulmonary stenosis etiology and anatomy

WikiDoc Microchapters for Pulmonary valve stenosis
Pulmonary valve stenosis Home Epidemiology and Demographics Etiology Anatomy
Diagnosis
Symptoms Physical Examination Echocardiography Severity Assessment
Treatment

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Etiology

• Congenital pulmonic stenosis is most common.

• Rheumatic involvement is rare, is usually part of multivalvular involvement, rarely leads to serious deformity.

• Carcinoid plaques can be present in the carcinoid syndrome. These result in constriction of the pulmonic valve ring, retraction and fusion of the valve cusps.

Anatomy

• Typically the valve is domed shaped with fused commissures.

• If the foramen ovale is patent, then right to left shunting can occur at the atrial level.

• If there is pulmonary atresia with an intact ventricular septum then these patients die soon after birth.