Noncompaction cardiomyopathy natural history
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Noncompaction Cardiomyopathy Microchapters |
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Pathophysiology |
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Differentiating Noncompaction Cardiomyopathy from other Diseases |
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Noncompaction cardiomyopathy natural history On the Web |
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Risk calculators and risk factors for Noncompaction cardiomyopathy natural history |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
The presence of NCC can also lead to other complications around the heart and in other organs. These are not necessarily common complications and no paper has yet to document the incidence of these complicationcs.
- Heart Related
- Abnormalities of the origin of the left coronary artery
- Pulmonary atresia
- Stenosis
- Right or Left ventricle obstruction
- Hypoplastic left ventricle
- Mitral regurgitation
- Tachyarrhythmias and sudden cardiac death
- Thrombus in the left ventricle
- Neuromuscular (Pertaining to both nerves and muscles)
- Genetic related
Prognosis
In so far as noncompaction cardiomyopathy is a recently described entity, its association with long term clinical outcomes is not known. In a 2005 study [1] which documented the long term follow up of 34 patients who were symptomatic with NCC, 35% had died at the age of 42 +/- 40 months. 12% of the patients required cardiac transplantation due to heart failure. However, this study was based upon symptomatic patients referred to a tertiary care center, and so were suffering from more severe forms of NCC than might be found typically in the population. As NCC is a genetic disease, as a precaution immediate family members are being tested which is turning up more supposedly healthy people with NCC who are not suffering from it. The long term prognosis for these people is currently unknown.
References
- ↑ Oechslin, Erwin; Jenni, Rolf (2005). "Non-compaction of the Left Ventricular Myocardium - From Clinical Observation to the Discovery of a New Disease" (webpage).