Noncompaction cardiomyopathy
| Noncompaction cardiomyopathy |
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Noncompaction Cardiomyopathy Microchapters |
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Pathophysiology |
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Differentiating Noncompaction Cardiomyopathy from other Diseases |
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Diagnosis |
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Treatment |
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Noncompaction cardiomyopathy On the Web |
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Risk calculators and risk factors for Noncompaction cardiomyopathy |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editors-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]
Synonyms and keywords: left ventricular noncompaction, LVNC, NCC, spongiform cardiomyopathy
Overview
Historical Perspective
Pathophysiology
Epidemiology
Natural History, Complications & Prognosis
Differentiating Noncompaction Cardiomyopathy other Diseases
Diagnosis
Symptoms
Echocardiography
Management
The management of NCC is similar to that of other cardiomyopathies and includes the use of ACE inhibitors, beta blockers and aspirin. Implantation of an automatic internal cardiac defibrillator AICD may be appropriate in patients who are deemed to be at increased risk of sudden cardiac death. A small study from the Netherlands identified young females with premature ventricular contractions (PVCs) at risk of sudden death[1].
In severe NCC cases, in which severe heart failure has developed, a heart transplant may be necessary.
Source
- "Left Ventriuclar noncompaction" (PDF). Orphanet.
See also
Barth syndrome, Emery-Dreifuss muscular dystrophy, myotubular myopathy, genes responsible for NCC are located also in the area that cause these conditions.