Rosai Dorfman disease
| Rosai-Dorfman disease | |
| Classification and external resources | |
| |
|---|---|
| Micrograph of a lymph node involved by Rosai-Dorfman disease showing emperipolesis. H&E stain. | |
| ICD-10 | D76.3 (ILDS D76.360) |
| DiseasesDB | 31419 |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Raviteja Guddeti, M.B.B.S. [2]
Synonyms and keywords: Sinus histiocytosis with massive lymphadenopathy, SHML, Destombes-Rosai-Dorfman syndrome, familial Rosai–Dorfman disease, familial SHML
Overview
Rosai–Dorfman disease is a rare disorder of unknown etiology that is characterized by abundant histiocytes in the lymph nodes throughout the body.[1]:747
- ↑ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.