Idiopathic interstitial pneumonia causes

Idiopathic interstitial pneumonias are broad subsets of pulmonary diseases due to unidentifiable causes. Therefore, the diagnosis of NSIP should lead to a careful clinical workup for the known etiological factors and possible adverse drug reaction before IIP is diagnosed.

The most common collagen vascular disease in the lung that should be excluded first are rheumatoid arthritis, systemic lupus erythematosus, Sjögren syndrome, polymyositis / dermatomyositis, progressive systemic sclerosis and mixed connective tissue disease.