Hamman-Rich syndrome: Difference between revisions

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{{DiseaseDisorder infobox |
{{Infobox disease |
   Name          = HR syndrome |
   Name          = Hamman–Rich syndrome |
   ICD10          = {{ICD10|J|84|1|j|80}} |
   ICD10          = {{ICD10|J|84|1|j|80}} |
   ICD9          = {{ICD9|516.3}} |
   ICD9          = {{ICD9|516.3}} |
   ICDO          = |
   ICDO          = |
   Image          = |
   Image          = Hyaline membranes - very high mag.jpg |
   Caption        = |
   Caption        = [[Micrograph]] of [[diffuse alveolar damage]], the histologic correlate of acute interstitial pneumonitis. [[H&E stain]]. |
   OMIM          = 178500 |
   OMIM          = 178500 |
   MedlinePlus    = |
   MedlinePlus    = |
Line 11: Line 11:
   eMedicineTopic = |
   eMedicineTopic = |
   DiseasesDB    = 4815 |
   DiseasesDB    = 4815 |
  MeshID        = D011658 |
}}
}}
{{SI}}


'''For patient information, click [[Hamman-Rich syndrome (patient information)|here]]'''
__NOTOC__
{{Hamman-Rich syndrome}}
{{CMG}}; {{AE}} {{CK}}


'''Hamman-Rich syndrome''' (also known as '''acute interstitial pneumonia''') is a rare, severe lung disease which usually affects otherwise healthy individuals.
{{SK}} Acute interstitial pneumonia; Acute interstitial pneumonitis; HR syndrome


HR syndrome is often categorized as both an [[interstitial lung disease]] and a form of [[acute respiratory distress syndrome]] (ARDS).
==[[Hamman-Rich syndrome overview|Overview]]==


== Symptoms ==
==[[Hamman-Rich syndrome historical perspective|Historical Perspective]]==
The most common symptoms of Hamman-Rich syndrome are [[cough]], [[fever]], and [[shortness of breath|difficulties breathing]]. These often occur over a period of one to two weeks before medical attention is sought. Difficulties breathing can quickly progress to an inability to breathe without support ([[respiratory failure]]).


Hamman-Rich syndrome typically progresses rapidly, with hospitalization and mechanical ventilation often required only days to weeks after initial symptoms of [[cough]], [[fever]], and [[shortness of breath|difficulties breathing]] develop.
==[[Hamman-Rich syndrome classification|Classification]]==


== Diagnosis ==
==[[Hamman-Rich syndrome pathophysiology|Pathophysiology]]==
Rapid progression from initial symptoms to respiratory failure is a key feature of Hamman-Rich syndrome. An x-ray which shows ARDS is necessary for diagnosis (fluid in the small air sacs ([[alveoli]]) in both lungs). In addition, a [[biopsy]] of the lung which shows organizing diffuse alveolar damage is required for diagnosis. Other diagnostic tests are useful excluding other similar condition, but history, x-ray, and biopsy are necessary. These other tests may include basic blood work, blood cultures, and [[bronchoalveolar lavage]].


== Treatment ==
==[[Hamman-Rich syndrome causes|Causes]]==
Treatment of HR syndrome is primarily supportive. Management in an [[intensive care unit]] is required and the need for [[mechanical ventilation]] is common. Therapy with [[corticosteroids]] is generally attempted, though their usefulness has not been established as of 2005.


== Epidemiology ==
==[[Hamman-Rich syndrome differential diagnosis|Differentiating Hamman-Rich syndrome from other Diseases]]==
HR syndrome occurs most frequently among people older than forty years old. It affects men and women equally. There are no known risk factors; in particular, [[tobacco smoking|smoking]] is not associated with increased risk.


== Prognosis ==
==[[Hamman-Rich syndrome epidemiology and demographics|Epidemiology and Demographics]]==
Sixty percent of people with HR syndrome will die in the first six months of illness. However, most people who have one episode do not have a second. People who survive often recover lung function completely.


== History ==
==[[Hamman-Rich syndrome risk factors|Risk Factors]]==
HR syndrome was first described in 1935 by [[Louis Hamman]] and Arnold Rich.


== References ==
==[[Hamman-Rich syndrome natural history, complications and prognosis|Natural History, Complications and Prognosis]]==
#{{note|Hamman}}  HR, AR. Fulminating diffuse interstitial fibrosis of the lungs. Trans Am Clin Climatol Assoc 1935; 51:154.


==External links==
==[[Hamman-Rich syndrome diagnosis|Diagnosis]]==
* {{WhoNamedIt|synd|3010}}
* {{Chorus|00181}}
* {{GPnotebook|1241907254}}
* {{FPnotebook|LUN100}}


{{Respiratory pathology}}
[[Hamman-Rich syndrome history and symptoms|History and Symptoms]] | [[Hamman-Rich syndrome physical examination|Physical Examination]] | [[Hamman-Rich syndrome laboratory findings|Laboratory Findings]] | [[Hamman-Rich syndrome electrocardiogram|Electrocardiogram]] | [[Hamman-Rich syndrome chest x ray|Chest X Ray]] | [[Hamman-Rich syndrome CT|CT]] | [[Hamman-Rich syndrome MRI|MRI]] | [[Hamman-Rich syndrome echocardiography or ultrasound|Echocardiography or Ultrasound]] | [[Hamman-Rich syndrome other imaging findings|Other Imaging Findings]] | [[Hamman-Rich syndrome other diagnostic studies|Other Diagnostic Studies]]
 
==Treatment==
 
[[Hamman-Rich syndrome medical therapy|Medical Therapy]] | [[Hamman-Rich syndrome surgery|Surgery]] | [[Hamman-Rich syndrome primary prevention|Primary Prevention]] | [[Hamman-Rich syndrome secondary prevention|Secondary Prevention]] | [[Hamman-Rich syndrome cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Hamman-Rich syndrome future or investigational therapies|Future or Investigational Therapies]]


==Case Studies==


[[Category:Pulmonology]]
[[Hamman-Rich syndrome case study one|Case #1]]


[[de:Akute interstitielle Pneumonie]]
{{Respiratory pathology}}
[[pt:Síndrome de Hamman-Rich]]
[[tr:Akut İnterstisyel Pnömoni]]


{{WikiDoc Help Menu}}
[[Category:Pulmonology]]
{{WikiDoc Sources}}

Latest revision as of 01:31, 25 March 2018

Hamman–Rich syndrome
Classification and external resources
Micrograph of diffuse alveolar damage, the histologic correlate of acute interstitial pneumonitis. H&E stain.
ICD-10 J84.1
ICD-9 516.3
OMIM 178500
DiseasesDB 4815
MeSH D011658

For patient information, click here

Hamman-Rich syndrome Microchapters

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Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Hamman-Rich syndrome from other Diseases

Epidemiology and Demographics

Risk Factors

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms

Physical Examination

Laboratory Findings

Electrocardiogram

Chest X Ray

CT

MRI

Echocardiography or Ultrasound

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Chandrakala Yannam, MD [2]

Synonyms and keywords: Acute interstitial pneumonia; Acute interstitial pneumonitis; HR syndrome

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Hamman-Rich syndrome from other Diseases

Epidemiology and Demographics

Risk Factors

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms | Physical Examination | Laboratory Findings | Electrocardiogram | Chest X Ray | CT | MRI | Echocardiography or Ultrasound | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical Therapy | Surgery | Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

Case Studies

Case #1

Template:Respiratory pathology

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