Peutz-Jeghers syndrome medical therapy

Peutz-Jeghers syndrome Microchapters
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Hamid Qazi, MD, BSc [2]

Overview

There is no medical treatment for Peutz-Jeghers syndrome. Depending on the associated cancer, radiotherapy or chemotherapy may be considered.

Medical Therapy

There is no medical treatment for Peutz-Jeghers syndrome. Depending on the associated cancer, radiotherapy or chemotherapy may be considered.

Patients with Peutz-Jeghers syndrome are treated with intra-operative enteroscopy (IOE) and double balloon enteroscopy (DBE).

• IOE
  • Laparotomy (laparoscopy) with endoscopy
  • Best modality for diagnostic and therapeutic procedure of the small bowel
• DBE
  • Allows examination and treatment of the Jejenum and Ileum

• Chemoprevention
  • Proven efficacy of rapamycin for Peutz-Jeghers syndrome in a mouse model

    

    By Veharan (Own work) [CC BY-SA 4.0 (https://creativecommons.org/licenses/by-sa/4.0)], via Wikimedia Commons